What is the survival rate for HLH?

What is the survival rate for HLH?

More recent studies have shown that the HLH-94 protocol resulted in an overall survival rate of 55%. Success or failure of an allogeneic BMT is the most important long-term prognostic factor. Unfortunately, many cases are diagnosed late in the course of the disease, after irreversible damage has occurred.

Can you recover from HLH?

Stem cell transplant can cure HLH in most cases. There is no way to prevent HLH, but as healthcare providers continue to learn more about it, treatment improves. Most children who are successfully treated go on to live normal lives.

Can an adult survive HLH?

Adult HLH is a rare and almost universally fatal disease entity without treatment with published median survival of 1.8–2.2 months.

How many people in the world have HLH?

HLH is a rare disease that affects about one in 50,000 births.

How long does it take to recover from HLH?

Long-Term Outlook Familial HLH is fatal without treatment, with median survival of about two to six months.

What is HLH?

What is HLH? You could save a life! If you, or someone you love, has been diagnosed with Hemophagocytic Lymphohistiocytosis (HLH), and you are trying to make sense of it all, then you have come to the right place. We understand the anguish and worry that comes with the diagnosis, and are here to help you navigate through the world of HLH.

What is the life expectancy of someone with HLH?

The genetic mutations that cause Primary HLH are present at birth, and patients often become ill with HLH in the first few years of life. If not detected and treated, primary HLH is usually fatal, typically within a few months.

Why choose hlhlh (Cambodia)?

HLH (Cambodia) Co., Ltd. Is committed to building long-term relationship based on integrity, performance, value and client satisfaction. We will continue to meet the changing needs of our clients with our quality services delivered by most qualified people.

Why are the numbers of HLH cases increasing?

These numbers seem to be increasing slightly, possibly due to increased success in detecting the disease. Primary HLH is caused by defects in several genes, including PRF1, UNC13D, STXBP2, STX11, RAB27A, LYST, AP3B1, SH2D1A, and XIAP/BIRC4.